ACYLGLYCINES, QUANTITATIVE

Test Documentation
Specimen Required
Collect random urine. Mix well and send 10.0 mL urine (4.0 mL minimum) frozen in a screw-capped plastic urine container.

Rejection Criteria
Non-frozen samples

Methodology
Gas Chromatography/Mass Spectrometry (GCMS) Stable Isotope Dilution Analysis

Stability
Room Temperature: Unacceptable; Refrigerated: 9 days; Frozen: 416 days

Reference Range
Ethylmalonic Acid   0.5-20.2 mg/g Cr  
2-Methylsuccinic Acid   0.4-13.8 mg/g Cr  
Glutaric Acid   0.6-15.2 mg/g Cr  
Isobutyrylglycine   0.00-11.0 mg/g Cr  
n-Butryrylglycine   0.1-2.1 mg/g Cr  
2-Methylbutyrylglycine   0.3-7.5 mg/g Cr  
Isovalerylglycine   0.3-14.3 mg/g Cr  
n-Hexanoylglycine   0.2-1.9 mg/g Cr  
n-Octanoylglycine   0.1-2.1 mg/g Cr  
3-Phenylpropionylglycine   0.00-1.1 mg/g Cr  
Suberylglycine   0.00-11.0 mg/g Cr  
trans-Cinnamoylglycine   0.2-14.7 mg/g Cr  
Dodecanedioic Acid (12.DCA)   0.00-1.1 mg/g Cr  
Tetradecanedioic Acid (14.DCA)   0.00-1.0 mg/g Cr  
Hexadecanedioic Acid (16.DCA)   0.00-1.0 mg/g Cr  

Performed
Monday, Wednesday, Friday

Turnaround Time7-16 days
Test CodeUACYQ
CPT-4 Code (s)
82542
LOINC Codes
Ethylmalonic Acid   13741-4  
2-Methylsoccinic acid   13777-8  
Glutaric acid   13748-9  
Isobutyrylglycine   38360-4  
n-Butyrylglycine   27892-9  
2-Methylbutyrylglycine   27097-5  
Isovalerylglycine   13766-1  
n-Hexanoylglycine   13753-9  
n-Octanoylglycine   38367-9  
3-Phenylpropionylglycine   13793-5  
Suberylglycine   13811-5  
trans-Cinnamoylglycine   38417-2  
Dodecanedioic acid   13732-3  
Tetradecanedioic acid   50333-4  
Hexadecanedioic acid   50332-6  
Interpretation   59462-2  
Reviewed by   No LOINC needed  

Warde
Medical
Laboratory